Volume 6, Issue 4, December 2020, Page: 459-462
The Quality of Life in Children with Hemophilia in Bali
I Gusti Ayu Trisna Windiani, Department of Child Health, Udayana University School of Medicine, Sanglah Hospital, Denpasar, Indonesia
Putu Antara, Department of Child Health, Udayana University School of Medicine, Sanglah Hospital, Denpasar, Indonesia
Soetjiningsih, Department of Child Health, Udayana University School of Medicine, Sanglah Hospital, Denpasar, Indonesia
I Gusti Agung Ngurah Sugitha Adnyana, Department of Child Health, Udayana University School of Medicine, Sanglah Hospital, Denpasar, Indonesia
Ketut Ariawati, Department of Child Health, Udayana University School of Medicine, Sanglah Hospital, Denpasar, Indonesia
Received: Mar. 4, 2020;       Accepted: Sep. 15, 2020;       Published: Nov. 11, 2020
DOI: 10.11648/j.ajp.20200604.22      View  29      Downloads  10
Abstract
Hemophilia in children adversely affects both their psychological as well as their physical health. It is important to understand more about the quality of life (QoL) in this patient population. The aim of this study was to assess health-related QoL of children with hemophilia in Bali. A cross sectional study was carried out on children with hemophilia in Bali. Data on the quality of life was collected through questionnaires using PedsQL Generic Core Scales version 4.0 inventory. Independent t test was used to analysis data. Child reports showed mean score on each domain function (physical, emotional, social and school function) in hemophilia group compared to healthy children group were 71.8 vs 97.9, 81.4 vs 94.5, 85.0 vs 97.5, and 73.1 vs 94.5, respectively. Parent-proxy reports showed mean scores on each domain function (physical, emotional, social, and school function) in hemophilia group compared to healthy children group were 73.3 vs 97.3, 79.5 vs 94.5, 80.2 vs 97.5, and 67.4 vs 89.8, respectively. Total PedsQL score in hemophilic children and healthy group showed a significant difference in both reports (child report; p<0.05, with the mean difference was -18.7 with 95% CI of -25.9 to -13.6 and parent-proxy report; p<0.05 the mean difference was -19.8 with 95% CI of -25.9 to -13.5). Hemophilia has a negative impact on the children’s daily life. Hemophilia group reported poor quality of life as regards the physical, emotional, social, school functioning domains, and total quality of life than healthy children group.
Keywords
Children, Hemophilia, Quality of Life
To cite this article
I Gusti Ayu Trisna Windiani, Putu Antara, Soetjiningsih, I Gusti Agung Ngurah Sugitha Adnyana, Ketut Ariawati, The Quality of Life in Children with Hemophilia in Bali, American Journal of Pediatrics. Vol. 6, No. 4, 2020, pp. 459-462. doi: 10.11648/j.ajp.20200604.22
Copyright
Copyright © 2020 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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